Hj ela tem severo atraso cognitivo e motor mas tenta se movimentar o tempo todo, as vezes tenta falar e muito risonha. As vezes tenta balbuciar algumas palavras. Enfim da gosto de ver. Aprendo com ela todos os dias. Porque Deus sabe de todas as coisas.

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Solicitud de separatas al Dr. Figura 1. En adultos con epilepsia secundaria generalizada, se ha descrito la existencia del SLG.

La edad promedio fue de Crisis convulsivas Los pacientes con SLG pueden presentar cualquier tipo de trastorno convulsivo. Puede existir compromiso de los pares craneanos, coreoatetosis y distonia, aunque es raro 5, 13, Figura 3.

Figura 4. El EEG demuestra descargada de punta-onda lenta a 1. Figura 5. El EEG de vigilia es generalmente desorganizado, excesivamente lento. Tabla 1. Retardo mental, en general. Se ha tenido buen resultado en pacientes con severo retardo mental y crisis convulsivas Su mayor efectividad se logra en el primer mes de tratamiento y especialmente en la segunda semana de iniciada la terapia. En general se recomiendan 20 a 40 U I.

Los resultados son en general pobres para los espasmos infantiles La dosis es de 0. ABSTRACT The Lennox-Gastaut syndrome is a well defined electroencephalographic and clinical entity displaying the following features: it occurs in children and less frequently in adolescents.

The association of several types of seizures, and the seizure type, are important criteria of clinical diagnosis. The most suggestive are atonic, tonic and atypical absences. Mental retardation is an essential component, although it may be absent at the onset of the syndrome. The most common EEG signs are bursts of diffuse slow-spike waves A brief history, etiology, symptons and signs, the EEG, the diagnosis, course, prognosis, and treatment are discussed by the authors.

The electroencephalogram in diagnosis and in localization of epileptic seizures. Arch Neurol Psychiat ; Influence of the bood sugar level on the wave and spike formation in petit mal epilepsy.

The Petit Mal epilepsis, their treatment with Tridione. JAMA ; 1. Clinical correlates of the fast and the slow spike-wave EEG. Pediatrics ; 5: Childhood epileptic encephalopathy with diffuse slow spike waves otherwise known as "Petit Malvariant" or Lennox syndrome. Epilepsia ; 7: The Lennox-Gastaut syndrome: a severe type of childhood epilepsy Abstract. F encephalogr Clin Neurophysiol ; The Generalized Epilepsies. Springfield: Thomas; Compendium of the Epilepsies, Springgield: Thomas; Basic principles, clinical applications and related.

Baltimore: Urban and Schwarzenberg; Comment on "Petit Mal variant" revisited. Epilepsia ; Petit Mal variant revisited. A case of Lennox-Gastaut syndrome successfully treated by removal of a parientotemporal astrocytoma. Childhood epileptic encephalopathy with slow spike wave. A statistical study of 80 cases. Epilepsis of infancy and childhood. Ann Neurol ; West syndrome and Lennox Gastaut syndrome: A survey of natural history. Pediatrics ; Slow spike-wave activity in EEG and associated clinical features: of ten called "Lennox" or "Lennox-Gastaut" syndrome.

Neurology ; Lennox syndrome. Europ Neurol ; 4: Lennox-Gastaut and lead intoxication. Genetics of Epilepsy: A review. New York: Raven Press; Myoclonus and the EEG, a review.

Clin Electroenceph ; Myoclonic Epilepsies. Therapy and Prognosis. Seventy adult cases with the Lennox-Gastaut syndrome Abstract. Epilepsy International Congress: Raven Press; Basel: Geigy; Typical and atypical epileptic absence seizures.

Advances in Epileptology. Myoclonic epilepsies in childhood. Myoclonic seizures: etiology and differential diagnosis. Current practice of clinical electroencephalography.

Complexities of primary generalized Epilepsy. Clin Electroeceph ; Absence of drug induced beta activity in the electroencephalogram. Europ Neurol ; Intravenous diazepam and its anticonvulsive action. Johns Hopkins Med ; Myoclonic seizures: Considerations in taxonomy.

New York: Raven Press, Sensory evoked potentials in the Lennox-Gastaut syndrome Abstract. Electroecephalogr Clin Neurophysiol ; Computerized transverse axial tomography in epilepsy. Lennox-Gastaut syndrome and computerized axial tomography findings. Positron emission tomography in two cases of chidhood epileptic encephalopathy Lennox Gastaut syndrome.

Neurology ; 1. JAMA ; Valproate sodium, effect in treatment of intractable epylepsy. Valproic acid. Arch Neurol ; The use of antiepileptic drugs. Ann Intern Med ; Valproic acid and intractable seizures in severely brain damaged patients. Phamacologic strategies in the treatment of epilepsy. Seminars in Neurol ; 1: Epilepsy in adults.

Ann Neurol ; 9: Arch Dis Child ; Drug therapy: clonazepam. N Engl J Med ; Aspecto electroclinico de las milclonias. Medium chain triglycerides as a therapy for intractable childhood epilepsy.


Síndrome de Lennox-Gastaut

When it recurs over and over, it is medically termed, epilepsy, which is a seizure disorder. The severe form of epilepsy is recognized as Lennox-Gastaut syndrome. It usually starts before a child turns 4-years-old. During this kind of seizure, the child suddenly falls to the ground, which may be mistaken as poor balance or tripping up. It usually happens many times in a day. Absences seizures An atypical seizure that last from 10 seconds to several minutes. The child usually stares blankly, appears vacant, and manifests rapid blinking or head nodding.


Lennox-Gastaut-Syndrom. Was ist das?

Was ist das Lennox-Gastaut-Syndrom? Es wird auch Lennox-Syndrom genannt und gilt als schwer behandelbar. Mitunter kommt es auch erst nach dem 8. Lebensjahr zum Ausbruch. Da es erhebliche Parallelen zum West-Syndrom gibt, wird eine Verwandtschaft zwischen beiden Erkrankungen vermutet.


Syndrome de Lennox-Gastaut


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